Ulman İ, Çelik A, Çetinkurşun S, Öztop F, Balık E. Pelvik

Transkript

Ulman İ, Çelik A, Çetinkurşun S, Öztop F, Balık E. Pelvik
pELviKRABDoMvoSARKoMA
oLGU
TEDAvisi
sonnestceg oONeuxotvtpr-ixAsyoNL.ARr:
SUNUMU
FS
O L L O W I NT
GR E A T M E NO
T F P E L V I CR H A B D O M Y C l J A ' i C C M
CA JE
LONG-TERC
MO M P L I C A T I O N
REPORT
l b r a h i mU L M A N T
A h m e tQ E L I K l
S a l i hQ E T I N K U R 9 U N l
F i k r i0 z T o P 2
FroltlALlK l
Trp Fak0ltesi,Bornova,lzmir
Ege Universitesi
l Q o c u kC e r r a h i sAi n a b i l i mD a l r
2 P a t o l oA
l i n a b i l i mD a l r
postradyasyon
Anahtar S6zcUkler:postradyasyon
komplikasyonlarr
sarkomu,rabdomyosarkom,
postradiation
Key Words: postradiation
complications
sarcoma,rhabdomyosarcoma,
OZET
Radyoterapive kemoterapinintedavidekietkinliQirabdomyosafuonta
rgin 6nenlencerrahi iglentlertlr..
or'r,tnl dt'r;ilthlt[.terr
neden olmugtur. Multidisiplineryaklaymlar sonucunda yagam oranlan eskiye oranla belirgin etritsg::::lermiglir Ancai
kemoterapiile birtikteolan radyasyonundzelliklegocuklarda1nemli yan etkileri gitr}lebilir. Bu galrgrnadaur,:yitlrnda tker
pelvik rabdomyosarkomtants alank bagarrltbir gekildetedavi edilen bir hastada, uzun sAre sortu ot!.iyi.)gri<t'tnvaJtrtit
Hastada tedavidenoniki ytl sonra orlaya Qtkanp():;traiir'asfons.trkctrnL,
okluzyonve sekondermaliQnNmdr tantmlanmtgtrr.
yumugakdoku fim6rlerinde uzun sureliizlemin 1nentinivurgulantaktadtr.
SUMMARY
The efficiencyof ndiation therapyand chemotherapyhas had a major impact on the surgicalproceduresre,comntenderi
fo
rhabdomyosarcoma.Wth multidisciplinaryregimens,survival rates have improved significantlyqontpareclto tltose in tht
past. However, radiation therapy in conjunction with chemotherapymay have deletenous side r,fecls i)at;,:Ltlarl',il
tor:i,t
children.In lhis repod,a case who presentedwith vaginalocclusion,and a secondarymalignantturrtctr
a[ler:;ucce]:;sn,
pelvic
treatmentof a
rhabdomyosarcomaat 3 years of age is descnbed.The impoftanceof long tenn {'::tlc'"';-u1.,
in sot li: -sr.i.
sarcomasof childhoodis emphasizedby this postradiationsarcomawhich has developedtwelve ytsr:, ,tfrarrttr ,tl trt'al
ment.
ciRig .
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y u m u g a k d o k u s a r k o m u v e t u m g o c u k l u kg a Q r m a l i g n ( 6 ) .A n c a kb u y t i k s e ky a g a mo r a n l a riil e b r i k t c ,t r o s t r a d , a s
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y a g t au y g u l a r r r r s ea k o n d etru m o rg e l r g m res k i o k a d a ra r l a r v a l i n a lo k l u z y o n ab a g l to l d L t Q cui L t g u r , rlrsr . r 1 r
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